Heterochromatin anomalies and double-stranded RNA accumulation underlie C9orf72 poly(PR) toxicity

Yong Jie Zhang, Lin Guo, Patrick K. Gonzales, Tania F. Gendron, Yanwei Wu, Karen Jansen-West, Aliesha D. O’Raw, Sarah R. Pickles, Mercedes Prudencio, Yari Carlomagno, Mariam A. Gachechiladze, Connor Ludwig, Ruilin Tian, Jeannie Chew, Michael DeTure, Wen Lang Lin, Jimei Tong, Lillian M. Daughrity, Mei Yue, Yuping SongJonathan W. Andersen, Monica Castanedes-Casey, Aishe Kurti, Abhishek Datta, Giovanna Antognetti, Alexander McCampbell, Rosa Rademakers, Björn Oskarsson, Dennis W. Dickson, Martin Kampmann, Michael E. Ward, John D. Fryer, Christopher D. Link, James Shorter, Leonard Petrucelli

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