TY - JOUR
T1 - Pseudomeningocele after in utero repair of myelomeningocele as an early sign of hypertensive hydrocephalus – a case report and review of the literature
AU - Cardeal, Daniel Dante
AU - Britto, Ingrid Schwach Werneck
AU - Herbst, Sandra Rejane Silva
AU - Toita, Milton Hikaru
AU - Bordini, Gabriela Duarte
AU - Veiga, José Carlos Esteves
AU - Ruano, Rodrigo
N1 - Publisher Copyright:
© 2021 by Cardeal et al. All rights reserved.
PY - 2022/1/1
Y1 - 2022/1/1
N2 - Background: Myelomenigocele (MMC) is the most common congenital defect of the spine. The Management of Myelomeningocele study (MOMS trial) demonstrated that the prenatal repair decreased shunt implant, reversal of hindbrain herniation and better neurologic function compared to postnatal repair. Several ultrasound findings can predict the risk of postnatal hydrocephalus after intrauterine MMC repair. This report shows a prenatal pseudomenigocele after intrauterine correction of MMC as an early sign of hydrocephalus. Method: A 34-year-old female G2P1 with a prenatal diagnosis of MMC with anatomical level L4 and ventricular enlargement was submitted to open surgery intrauterine repair. Follow up ultrasound showed regression of the lemon sign, partial regression of hindbrain herniation and a progressive increase in the wound with local bulging characterizing a pseudomingocele. In the postnatal period, after correction of the pseudomenigocele, the neonate showed signs of hipertensive hydrocephalus. After ventriculoperitoneal shunt, the patient was discharged. Conclusion: Presence of pseudomeningocele prenatally after in utero repair of MMC may represent an early sign of hypertensive hydrocephalus.
AB - Background: Myelomenigocele (MMC) is the most common congenital defect of the spine. The Management of Myelomeningocele study (MOMS trial) demonstrated that the prenatal repair decreased shunt implant, reversal of hindbrain herniation and better neurologic function compared to postnatal repair. Several ultrasound findings can predict the risk of postnatal hydrocephalus after intrauterine MMC repair. This report shows a prenatal pseudomenigocele after intrauterine correction of MMC as an early sign of hydrocephalus. Method: A 34-year-old female G2P1 with a prenatal diagnosis of MMC with anatomical level L4 and ventricular enlargement was submitted to open surgery intrauterine repair. Follow up ultrasound showed regression of the lemon sign, partial regression of hindbrain herniation and a progressive increase in the wound with local bulging characterizing a pseudomingocele. In the postnatal period, after correction of the pseudomenigocele, the neonate showed signs of hipertensive hydrocephalus. After ventriculoperitoneal shunt, the patient was discharged. Conclusion: Presence of pseudomeningocele prenatally after in utero repair of MMC may represent an early sign of hypertensive hydrocephalus.
KW - Arnold-Chiari Malformation
KW - Fetal Surgery
KW - Hydrocephalus
KW - Myelomeningocele
KW - Prenatal Diagnosis
KW - Ventriculoperitoneal Shunt
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U2 - 10.46900/apn.v4i1(January-April).103
DO - 10.46900/apn.v4i1(January-April).103
M3 - Article
AN - SCOPUS:85183869932
SN - 2675-3626
VL - 4
JO - Archives of Pediatric Neurosurgery
JF - Archives of Pediatric Neurosurgery
IS - 1
M1 - e1032021
ER -