Immunoglobulin G4 (IgG4) Related Disease

Krati Chauhan; Phil A. Hart; Vaidehi R. Chowdhary

doi:10.1007/978-1-4614-5088-7_5

Immunoglobulin G4 (IgG4) Related Disease

Krati Chauhan, Phil A. Hart, Vaidehi R. Chowdhary

Rheumatology

Research output: Chapter in Book/Report/Conference proceeding › Chapter

Abstract

IgG4-related disease (IgG4-RD) is a recently recognized syndrome characterized by frequent elevation of serum Ig4 levels and typical pathology of the affected organs. Biopsy shows lymphoplasmacytic inflammation, frequent eosinophils, storiform fibrosis, obliterative phlebitis and abundant IgG4-positive staining plasma cells. Disease manifestations often respond dramatically to steroid therapy.

Original language	English (US)
Title of host publication	Challenging Cases in Rheumatology and Diseases of the Immune System
Publisher	Springer New York
Pages	73-88
Number of pages	16
ISBN (Electronic)	9781461450887
ISBN (Print)	146145087X, 9781461450870
DOIs	https://doi.org/10.1007/978-1-4614-5088-7_5
State	Published - Mar 1 2014

Keywords

Aortitis
Autoimmune pancreatitis
IgG4
Orbital pseudolymphoma

ASJC Scopus subject areas

General Medicine

Access to Document

10.1007/978-1-4614-5088-7_5

Cite this

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AU - Hart, Phil A.

AU - Chowdhary, Vaidehi R.

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PY - 2014/3/1

Y1 - 2014/3/1

N2 - IgG4-related disease (IgG4-RD) is a recently recognized syndrome characterized by frequent elevation of serum Ig4 levels and typical pathology of the affected organs. Biopsy shows lymphoplasmacytic inflammation, frequent eosinophils, storiform fibrosis, obliterative phlebitis and abundant IgG4-positive staining plasma cells. Disease manifestations often respond dramatically to steroid therapy.

AB - IgG4-related disease (IgG4-RD) is a recently recognized syndrome characterized by frequent elevation of serum Ig4 levels and typical pathology of the affected organs. Biopsy shows lymphoplasmacytic inflammation, frequent eosinophils, storiform fibrosis, obliterative phlebitis and abundant IgG4-positive staining plasma cells. Disease manifestations often respond dramatically to steroid therapy.

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KW - Autoimmune pancreatitis

KW - IgG4

KW - Orbital pseudolymphoma

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BT - Challenging Cases in Rheumatology and Diseases of the Immune System

PB - Springer New York

ER -

Immunoglobulin G4 (IgG4) Related Disease

Abstract

Keywords

ASJC Scopus subject areas

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