Abstract
Orthotopic liver transplantation for other diseases typically results in a coincidental cure for hemophilia A and B; however, long-term outcomes of liver transplant in hemophilia C are not very well described. Herein, the authors report a patient of severe congenital factor XI (FXI) deficiency who received an orthotopic liver transplant. The authors discuss the perioperative management and long-term outcomes. The normalization of his FXI levels confirms that the liver is the most clinically relevant site of synthesis of FXI.
Original language | English (US) |
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Pages (from-to) | 961-963 |
Number of pages | 3 |
Journal | Blood Coagulation and Fibrinolysis |
Volume | 26 |
Issue number | 8 |
DOIs | |
State | Published - 2015 |
Keywords
- Bleeding
- Clotting factors
- Factor XI deficiency
- Hemophilia
- Liver transplant
ASJC Scopus subject areas
- Hematology