Congenital cystic adenomatoid malformation

David Levin, Thomas Hartman

Research output: Chapter in Book/Report/Conference proceedingChapter


Imaging description Congenital cystic adenomatoid malformations (CCAMs) account for 25% of all congenital lung abnormalities. CCAMs are divided into three types: type 1 consists of cysts between 2 cm and 10 cm in diameter; type 2 consists of cysts between 0.5 cm and 2 cm in diameter; and type 3 consists of microscopic cysts [1–3]. Most lesions are identified within the first two years of life. However, in the rare cases where the lesions are not identified until adulthood, they are usually either type 1 or type 2 CCAMs. On imaging, type 1 CCAMs are most commonly a large cyst (up to 12 cm in diameter) or a few cysts, possibly containing air/fluid levels. Type 2 CCAMs are typically multicystic (2–20 mm in diameter) and may also contain air/fluid levels (Figure 14.1). CCAMs typically exhibit mass effect on the adjacent lung and when large enough can displace mediastinal structures. They are most commonly seen in the lower lobes and are surrounded by “normal” lung parenchyma. Importance CCAMs are a common congenital lesion of the lung and should be considered in the differential of pulmonary lesions detected in early childhood or prenatally. In the adult, the lesions are a cause of recurrent infection.

Original languageEnglish (US)
Title of host publicationPearls and Pitfalls in Thoracic Imaging
Subtitle of host publicationVariants and Other Difficult Diagnoses
PublisherCambridge University Press
Number of pages2
ISBN (Electronic)9780511977701
ISBN (Print)9780521119078
StatePublished - Jan 1 2011

ASJC Scopus subject areas

  • General Medicine


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