TY - JOUR
T1 - Autoimmune myelofibrosis with pancytopenia as a presenting manifestation of systemic lupus erythematosus responsive to mycophenolate mofetil
AU - Ungprasert, Patompong
AU - Chowdhary, V. R.
AU - Davis, M. D.
AU - Makol, Ashima
PY - 2016/4/1
Y1 - 2016/4/1
N2 - Hematological abnormalities, such as anemia, leucopenia, and thrombocytopenia, secondary to peripheral destruction, are common in systemic lupus erythematosus (SLE). However, cytopenias from autoimmune myelofibrosis (AIMF) are extremely uncommon in SLE, with less than 40 reported cases in the literature. We report the case of a 33-year-old female who presented with bullous skin lesions and pancytopenia as the presenting manifestation of what was ultimately diagnosed as SLE with AIMF. She responded well to glucocorticoids and mycophenolate mofetil.
AB - Hematological abnormalities, such as anemia, leucopenia, and thrombocytopenia, secondary to peripheral destruction, are common in systemic lupus erythematosus (SLE). However, cytopenias from autoimmune myelofibrosis (AIMF) are extremely uncommon in SLE, with less than 40 reported cases in the literature. We report the case of a 33-year-old female who presented with bullous skin lesions and pancytopenia as the presenting manifestation of what was ultimately diagnosed as SLE with AIMF. She responded well to glucocorticoids and mycophenolate mofetil.
KW - cutaneous lupus
KW - hematologic changes
KW - Systemic lupus erythematosus
UR - http://www.scopus.com/inward/record.url?scp=84960441019&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84960441019&partnerID=8YFLogxK
U2 - 10.1177/0961203315615221
DO - 10.1177/0961203315615221
M3 - Article
C2 - 26537421
AN - SCOPUS:84960441019
SN - 0961-2033
VL - 25
SP - 427
EP - 430
JO - Lupus
JF - Lupus
IS - 4
ER -