Arrhythmias and arrhythmia management in hypertrophic cardiomyopathy

J. Martijn Bos, Steve R. Ommen, Michael J. Ackerman

Research output: Chapter in Book/Report/Conference proceedingChapter


Cardiomyopathies are diseases of the myocardium associated with cardiac dysfunction. According to the World Health Organization (WHO) classification, cardiomyopathies are classified either as primary or secondary cardiomyopathies. Based on morphological and functional criteria, heritable cardiomyopathies are classified into four primary categories including hypertrophic cardiomyopathy (HCM), dilated cardiomyopathy (DCM), arrhythmogenic right ventricular cardiomyopathy (ARVC), and restrictive cardiomyopathy (RCM). More recently, left ventricular non-compaction (LVNC) syndrome has been recognized as a separate cardiomyopathy. Secondary cardiomyopathies include for example ischemic and hypertensive cardiomyopathy. This chapter focuses solely on HCM, the most common heritable cardiovascular disease (estimated prevalence 1:500) and the most common cause of sudden cardiac death (SCD) in young adolescents and athletes. This chapter discusses HCM's clinical and genetic substrate, genetic testing and screening, and has particular focus on its arrhythmogenic features and the role and indication of the implantable cardioverter defibrillator (ICD) and prevention of SCD.

Original languageEnglish (US)
Title of host publicationDiagnosis and Treatment
PublisherSpringer-Verlag London Ltd
Number of pages18
ISBN (Electronic)9781447149781
ISBN (Print)1447149777, 9781447149774
StatePublished - Jul 1 2013


  • Genetics
  • HCM
  • Hypertrophic cardiomyopathy
  • ICD
  • Sudden cardiac death

ASJC Scopus subject areas

  • General Medicine


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