Anesthesia for patients with congenital long QT syndrome

Susan J. Kies, Christina M. Pabelick, Heather A. Hurley, Roger D. White, Michael J. Ackerman

Research output: Contribution to journalReview articlepeer-review

101 Scopus citations


Long QT syndrome is a malfunction of cardiac ion channels resulting in impaired ventricular repolarization that can lead to a characteristic polymorphic ventricular tachycardia known as torsades de pointes. Stressors, by increasing sympathetic tone, and drugs can provoke torsade de pointes, leading to syncope, seizures, or sudden cardiac death in these patients. Beta blockade, implantation of cardioverter defibrillators, and left cardiac sympathetic denervation are used in the treatment of these patients. However, these treatment modalities do not guarantee the prevention of sudden cardiac death. Certain drugs, including anesthetic agents, are known to contribute to QT prolongation. After reviewing the literature the authors give recommendations for the anesthetic management of these patients in the perioperative period.

Original languageEnglish (US)
Pages (from-to)204-210
Number of pages7
Issue number1
StatePublished - Jan 2005

ASJC Scopus subject areas

  • Anesthesiology and Pain Medicine


Dive into the research topics of 'Anesthesia for patients with congenital long QT syndrome'. Together they form a unique fingerprint.

Cite this