Cerebral Microvascular Erdheim-Chester Disease: A Perivascular Hematopoietic Vasculopathy

Michael Moussouttas, Shanu Roemer, Dennis W. DIckson

Research output: Contribution to journalArticlepeer-review


Erdheim-Chester disease (ECD) is a rare and elusive hematopoietic malignancy that may involve the nervous system in various ways. Cerebrovascular ECD involves the perivascular infiltration and compromise of any cervicocranial vessel by transformed proliferating histiocytes. Presented is the novel case of a patient with pathologically proven perivascular microangiopathy, manifesting in multifaceted fashion with ischemia, hemorrhage, mass lesions, and edema.

Original languageEnglish (US)
Pages (from-to)746-751
Number of pages6
JournalCerebrovascular Diseases
Issue number6
StatePublished - Dec 1 2021


  • Autopsy
  • Cerebral vasculature
  • Erdheim-Chester disease
  • Hemorrhage
  • Infarction
  • Microvascular infiltrates
  • Perivascular microangiopathy

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology
  • Cardiology and Cardiovascular Medicine


Dive into the research topics of 'Cerebral Microvascular Erdheim-Chester Disease: A Perivascular Hematopoietic Vasculopathy'. Together they form a unique fingerprint.

Cite this