Catecholaminergic polymorphic ventricular tachycardia

Research output: Chapter in Book/Report/Conference proceedingChapter


Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a rare genetic disorder characterized clinically by adrenergically triggered syncope and sudden cardiac death. Although the resting 12-lead electrocardiogram is typically normal in CPVT, the presence of exercise- or catecholamine infusion-triggered premature ventricular contractions occurring in bigeminy and/or couplets as well as, in rare circumstances, in bidirectional/polymorphic ventricular tachycardia serves as the primary hallmarks of CPVT electrocardiographically. In this chapter, we examine these key electrocardiographic findings and the associated pathophysiology that gives rise to these findings at the cellular, tissue, and/or organ level.

Original languageEnglish (US)
Title of host publicationElectrocardiography of Inherited Arrhythmias and Cardiomyopathies
Subtitle of host publicationFrom Basic Science to Clinical Practice
PublisherSpringer International Publishing
Number of pages12
ISBN (Electronic)9783030521738
ISBN (Print)9783030521721
StatePublished - Sep 21 2020


  • CPVT
  • ECG
  • SCD

ASJC Scopus subject areas

  • General Medicine


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